Macrodactyly with skin hypertrophy: a minimal form of the Proteus syndrome.

نویسندگان

  • Hiram Larangeira de Almeida
  • Roberto Coswig Fiss
  • Rudolf Happle
چکیده

The Proteus syndrome was described 1983 . It has asymmetric gigantism of the limbs, verrucous epidermal naevi, cerebriform enlargement of the plantar region, vascular malformations and neoplasms, as lipomas. It received this denomination after Proteus from the Greek mythology, who had the ability to change his form . A 15 year-old boy, reported a congenital hypertrophy with syndactily of the second and third right fingers . The second case is a 35 year-old man, who reported that since birth the second right toe was bigger than the other toes, skin hypertrophy was also observed. These cases document a localized form if the Proteus syndrome, which may widen the spectrum of its variability.

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Proteus syndrome: A case report

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عنوان ژورنال:
  • Anais brasileiros de dermatologia

دوره 86 3  شماره 

صفحات  -

تاریخ انتشار 2011